Malignant pigmented clear cell epithelioid cell tumor (PEComa) in an adolescent boy with widespread metastases: A rare entity in this age group
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摘要Malignant pigmented clear cell epithelioid cell tumor of the kidney is a rare variant of perivascular epithelioid cells tumors (PEComa) or epithelioid angiomyolipoma (AML). PEComa is characteristically composed purely of epitheloid cells. The fat cells and the blood vessels that are typical of classic AML are absent. Most epithelioid AML cases are benign; however, malignant epithelioid AML of the kidney has been occasionally reported in adults in association with tuberous sclerosis. We report the radiological-pathological features of a malignant pigmented clear cell epithelioid renal tumor in a 15-year-old boy presenting with extensive metastases but without clinical evidence of tuberous sclerosis. © 2011 Springer-Verlag.
著者Rasalkar D.D., Chu W.C.-W., Chan A.W.H., Cheng F.W.T., Li C.K.
期刊名稱Pediatric Radiology
出版年份2011
月份12
日期1
卷號41
期次12
出版社Springer Verlag
出版地Germany
頁次1587 - 1590
國際標準期刊號0301-0449
語言英式英語
關鍵詞Adolescent, Kidney, Pigmented epitheloid tumor

上次更新時間 2020-28-10 於 02:50